Biology • Year 12 • Module 6 • Lesson 3

Point Mutation — Base-Level Genetic Change

Apply substitution / insertion / deletion reasoning to a codon table, the sickle-cell missense classic, and three real point-mutation examples.

Apply · Codon Tables & Case Studies

1. Use the codon table — predict the protein consequence

The simplified mRNA codon table below shows codons read 5′→3′. Use it for all five sub-questions. 8 marks

            2nd base
1st base    U                   C                   A                   G              3rd base
  U     UUU/UUC Phe         UCU/UCC/UCA/UCG     UAU/UAC Tyr         UGU/UGC Cys        U / C
        UUA/UUG Leu             Ser             UAA/UAG STOP         UGA STOP / Trp     A / G
  C     CUU/CUC/CUA/CUG     CCU/CCC/CCA/CCG     CAU/CAC His         CGU/CGC/CGA/CGG    U / C
            Leu                 Pro             CAA/CAG Gln              Arg            A / G
  A     AUU/AUC/AUA Ile     ACU/ACC/ACA/ACG     AAU/AAC Asn         AGU/AGC Ser        U / C
        AUG Met (Start)         Thr             AAA/AAG Lys         AGA/AGG Arg         A / G
  G     GUU/GUC/GUA/GUG     GCU/GCC/GCA/GCG     GAU/GAC Asp         GGU/GGC/GGA/GGG    U / C
            Val                 Ala             GAA/GAG Glu              Gly            A / G

1.1 Original mRNA codon GAA → mutant codon GAG. Identify the type of point mutation and the codon-level outcome (silent / missense / nonsense). Justify using the table. 2 marks

1.2 Original codon UGG (Trp) → mutant codon UGA. Identify the type and codon-level outcome, and predict the effect on the polypeptide. 2 marks

1.3 Original codon GAA → mutant codon GUA. Identify the type and codon-level outcome, and state precisely how the amino acid changes. 2 marks

1.4 An mRNA reads AUG | AAA | CCU | GGA | UUU | UAA. A single base is inserted after the start codon, giving AUG | XAA | ACC | UGG | AUU | UUA | A... where X is any base. State (i) what type of point mutation this is, and (ii) what happens to the protein, with reference to the reading frame. 2 marks

Stuck? Read codons 5′→3′. Silent = same amino acid; missense = different amino acid; nonsense = stop codon. Single-base indel = frameshift downstream.

2. Sickle-cell anaemia — the classic missense case

Sickle-cell anaemia is caused by a single point mutation in the gene coding for the β-globin chain of haemoglobin. The first seven codons of the normal and mutant mRNA are shown below. 9 marks

β-globin codons 1–7    1 (Met)  2 (Val)  3 (His)  4 (Leu)  5 (Thr)  6        7 (Glu)
Normal HbA mRNA        AUG  |   GUG  |  CAC  |  CUG  |  ACU  |  GAG  |  GAG
Mutant HbS mRNA        AUG  |   GUG  |  CAC  |  CUG  |  ACU  |  GUG  |  GAG
                                                                    ↑
                                                  position 6: middle A → U (single substitution)

2.1 Identify the type of point mutation and the codon-level outcome shown by the HbS mutation. 2 marks

2.2 Using the codon table from Section 1, state which amino acid replaces which at position 6, and write out the first seven amino acids of HbS. 2 marks

2.3 Glutamate (Glu) has a charged, polar side chain; valine (Val) has an uncharged, non-polar side chain. Explain how this single amino-acid change alters the behaviour of haemoglobin and the shape of the red blood cell. 3 marks

2.4 Use the sickle-cell example to refute the misconception "if only one base changes, only a small thing in the body changes". 2 marks

Stuck? Walk the DNA → codon → amino acid → protein behaviour → red cell shape chain explicitly.

3. Classify three real point-mutation examples

The table below summarises three real point mutations seen in HSC-level Biology contexts. For each row complete columns (a)–(c). 9 marks (3 marks per row)

Example Sequence-level change (mRNA) (a) Type (b) Codon-level outcome (c) Likely protein effect
3.1 Cystic fibrosis (most common allele, ΔF508) in the CFTR gene of chloride-channel protein. Three bases deleted; codon for phenylalanine at position 508 is removed entirely, reading frame downstream unchanged.
3.2 Duchenne muscular dystrophy in DMD (dystrophin) — example single-base deletion early in the coding sequence. One base deleted near the start of the coding sequence, regrouping all later codons and introducing an early UAA in roughly the 20th codon downstream.
3.3 Tay–Sachs disease (one well-known allele) in HEXA coding for β-hexosaminidase A. Single base substitution converts a CGA (Arg) codon into UGA, terminating translation before the catalytic domain is complete.
Stuck? Match each scenario to the same logic used in Sections 1–2: deletion of three bases ≠ frameshift; single-base deletion = frameshift; substitution into a STOP codon = nonsense.

4. Interpret data — protein length vs frameshift position

A research team artificially induced single-base deletions at five different positions along a 480-amino-acid enzyme. They measured the length of the polypeptide produced (in amino acids) before translation terminated, in each mutant. 6 marks

0 100 200 300 400 500 Polypeptide length produced (amino acids) Codon position where single base was deleted wild-type = 480 aa 26 codon 20 91 codon 80 213 codon 200 358 codon 350 474 codon 470

Stylised data — each bar is a separate experimental mutant; the dashed line shows the wild-type protein length (480 aa).

4.1 Describe the relationship between the codon position of the single-base deletion and the resulting polypeptide length. 2 marks

4.2 Explain why a frameshift near codon 20 produces a much shorter polypeptide than a frameshift near codon 470. 2 marks

4.3 Which mutant would you predict to retain the most enzyme function, and why? 2 marks

Stuck? Frameshifts regroup every downstream codon, so an early frameshift usually generates a premature stop codon by chance very soon after the mutation site.
Answers — Do not peek before attempting

Q1.1 — GAA → GAG

Type: substitution. Codon-level outcome: silent. GAA and GAG both code for glutamate (Glu), so the amino acid does not change and the protein sequence is unaltered.

Marking notes. 1 mark for substitution; 1 mark for silent with explicit reference to the codon table (both code Glu).

Q1.2 — UGG → UGA

Type: substitution. Codon-level outcome: nonsense. UGG (Trp) becomes UGA, a stop codon, so the ribosome terminates translation at this codon and the polypeptide is truncated, typically losing function.

Marking notes. 1 mark for substitution; 1 mark for nonsense with reference to STOP and truncation.

Q1.3 — GAA → GUA

Type: substitution. Codon-level outcome: missense. GAA codes for glutamate (Glu) and GUA codes for valine (Val), so one amino acid in the polypeptide is replaced with a chemically different one.

Marking notes. 1 mark for substitution; 1 mark for missense plus explicit Glu→Val.

Q1.4 — Single-base insertion after AUG

(i) Insertion; (ii) the reading frame is shifted by one base from codon 2 onward, so every downstream codon is regrouped — almost every amino acid after the mutation is changed and a premature stop codon (UAA in codon 6 of the mutant: U|UAA) terminates translation early. This is a frameshift at the codon-outcome level.

Marking notes. 1 mark for insertion; 1 mark for explicit "frameshift / reading frame shifted, premature stop".

Q2.1 — Sickle-cell type and outcome

Type: substitution (one base of one codon is changed). Codon-level outcome: missense — the new codon codes for a different amino acid.

Marking notes. 1 mark per correct identification (substitution, missense).

Q2.2 — Amino-acid change and first seven amino acids of HbS

At codon 6 the codon changes from GAG (Glu) to GUG (Val), so glutamate is replaced by valine. The first seven amino acids of HbS are: Met – Val – His – Leu – Thr – Val – Glu.

Marking notes. 1 mark for Glu → Val at position 6; 1 mark for correctly writing the first seven residues with the substitution incorporated.

Q2.3 — Why the single substitution matters

Replacing the charged, polar glutamate with a non-polar valine introduces a hydrophobic patch on the surface of haemoglobin. Under low-oxygen conditions, the non-polar valine residues on adjacent haemoglobin molecules associate, causing the haemoglobin to polymerise into long fibres inside the red blood cell. These fibres distort the cell from a flexible biconcave disc into the rigid, sickle-shaped form characteristic of the disease, blocking capillaries and reducing oxygen delivery.

Marking notes. 1 mark for explicit charge/polarity change (Glu polar/charged → Val non-polar/hydrophobic); 1 mark for polymerisation/aggregation of haemoglobin under low-O₂; 1 mark for the link to red blood cell shape change.

Q2.4 — Refuting the misconception

The sickle-cell case shows that a single base substitution in the β-globin gene, which changes only one amino acid out of 146 in the β chain, can produce haemoglobin that polymerises under low oxygen, deforms red blood cells, blocks capillaries, and causes a serious clinical phenotype — anaemia, pain crises and organ damage. A one-base change can therefore have a major biological effect when it lands in a functionally critical position.

Marking notes. 1 mark for stating that the DNA change is tiny (single base / one amino acid); 1 mark for connecting that small change to a major phenotype consequence.

Q3 — Three real point-mutation examples

3.1 Cystic fibrosis ΔF508: (a) Deletion (three bases / one codon); (b) not a frameshift — one entire codon is removed, so the reading frame is preserved and the rest of CFTR is translated normally; (c) the CFTR chloride channel is missing one phenylalanine, misfolds in the ER, and is degraded before reaching the cell membrane — chloride/water transport across epithelia fails.

3.2 Duchenne muscular dystrophy (single-base deletion): (a) Deletion; (b) frameshift — every codon after the deletion is regrouped and a premature stop codon appears about 20 codons downstream; (c) the dystrophin protein is severely truncated, missing almost all of its functional domains, so it cannot stabilise the muscle fibre membrane — progressive muscle degeneration follows.

3.3 Tay–Sachs (CGA → UGA): (a) Substitution; (b) nonsense — CGA (Arg) becomes UGA (STOP); (c) β-hexosaminidase A is truncated before its catalytic site is completed, has no enzyme activity, and GM2 gangliosides accumulate in neurons, causing neurodegeneration.

Marking notes. 1 mark per column ((a) type, (b) codon-level outcome, (c) protein effect) per row; max 9. For 3.1, the (b) answer must explicitly note "no frameshift / reading frame preserved because three bases = one codon".

Q4.1 — Trend

As the codon position of the deletion moves further along the gene, the resulting polypeptide length increases. The relationship is approximately linear: in each case the polypeptide stops a few amino acids downstream of the deletion site (codon 20 → 26 aa, codon 80 → 91 aa, codon 200 → 213 aa, codon 350 → 358 aa, codon 470 → 474 aa). None reach the wild-type length of 480.

Marking notes. 1 mark for "positive / increasing" relationship; 1 mark for using at least two data points or quoting that translation stops a few codons after the deletion in every case.

Q4.2 — Why an early frameshift gives a short polypeptide

A single-base deletion shifts the reading frame, so every codon downstream is regrouped. Across a random sequence, one of the three stop codons (UAA, UAG or UGA) appears by chance roughly every 21 codons on average, so a frameshift introduced near the start of the gene almost always generates a premature stop very soon after the deletion site. A frameshift near codon 470 has only ~10 codons of original sequence left before the natural stop, so the truncation is small.

Marking notes. 1 mark for "frameshift regroups downstream codons"; 1 mark for "stop codon appears by chance soon after deletion, so the polypeptide ends a few residues later".

Q4.3 — Most-functional mutant

The deletion at codon 470 would retain the most function. Its polypeptide is 474 amino acids — only 6 fewer than wild-type — and almost the entire enzyme, including the catalytic and folding regions, is still present. Active-site geometry and most structural features should be largely intact, so residual function is most likely.

Marking notes. 1 mark for choosing the codon-470 mutant; 1 mark for justification referring to almost-complete length / active site preserved.